| CASE REPORT |
|
| Year : 2008 | Volume
: 45
| Issue : 2 | Page : 64-66 |
Wunderlich's syndrome with hepatic angiomyolipoma in tuberous sclerosis
R Mongha, P Bansal, A Dutta, RK Das, AK Kundu
Department of Urology, Institute of Post Graduate Medical Education and Research, Kolkata, India
Correspondence Address:
R Mongha
Department of Urology, Institute of Post Graduate Medical Education and Research, Kolkata
India
DOI: 10.4103/0019-509X.41773 PMID: 18626151
We present a patient of tuberous sclerosis complex with bilateral renal angiomyolipoma and hepatic angiomyolipoma with spontaneous retroperitoneal hemorrhage from right angiomyolipoma (Wunderlich's syndrome). Nephron preserving approach was tried but the right kidney could not be salvaged. Hepatic angiomyolipoma was managed conservatively. Wunderlich's syndrome has been found in around 10% of cases of renal angiomyolipomas. Hepatic Angiomyolipoma is a benign mesenchymal neoplasm of the liver which is rarely reported in literature
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